Table 6.

Progressive Hearing Loss in Individuals With Cx26 Mutations

MutationIndividualAge First Audiogram (Years)Number of Years FollowedIPHL dB/YearTotal Change mPTA dB
35delG 748-41072.618.2
35delG1560-2163.923.4
35delG1579-12112.830.8
35delG1586-2825.010.0
35delG1750-151211.429.4
167delT1428-21063.420.4
167delT2084-1581.08.0
35delG/250G>C1612-1431.03.0
167delT/631–632del1692-1525.310.6
35delG/314–327del1852-1642.710.8