STOKES-ADAMS SYNDROME ASSOCIATED WITH COMPLETE CONGENITAL HEART BLOCK IN INFANCY AND CHILDHOOD

Abstract

Complete congenital heart block with syncopal or convulsive seizure reaction (Stokes-Adams syndrome), although a rare condition, requires differentiation from other types of fainting spells and convulsive disorders of infancy and childhood. Symptoms of this syndrome, aside from the cerebral manifestations, are few.

Stokes-Adams attacks represent an emergency because of the possibility of sudden death. Congenital heart block without attacks is compatible with a normal life expectancy.

Stokes-Adams syndrome in this case seemed to be precipitated by mild respiratory infections and over-exertion. Asymmetric deviations of cervical pulsations, facial contour and EEG tracings were noted.