TABLE 1

Extracutaneous Changes Associated With Linear Scleroderma en coup de sabre and Parry-Romberg Syndrome

Neurologic
    Seizure disorder, typically complex partial3,5,8,20,2729a
    Hemiparesis/muscle weakness4,9,17a
    Trigeminal neuralgia3a
    Intracranial aneurysm30a
    Rasmussen encephalitis31a
    Mental deterioration28a
    Subdural hygroma29a
    Peripheral facial nerve palsy19
    Oculomotor nerve palsy19
    Migraine headaches3
Ophthalmologic
    Ptosis3,8,12,19,32a
    Exophthalmos3a
    Uveitis3,8a
    Motility disorder/atrophy of eye muscles32a
    Heterochromia of iris32,33
    Papillitis8
    Retrobulbar pain8
    Enophthalmus34
    Displacement of outer canthus from resorption of orbital bone3
    Iridocyclitis7
Oral
    Altered dentition3,14,29,33a
    Malocclusion3a
    Tongue atrophy3,14,33a
  • a Changes reported in pediatric patients.