Table 2.

Prevalence and Distribution of Major Congenital Heart Defects by Race, Metropolitan Atlanta, 1968–1997

Defect TypeWhitesBlacksRate
Ratio
95% Confidence
Interval
PRate
Difference§
No.%Rate*No.%Rate
Heterotaxias391.20.71381.71.111.550.99–2.420.4
Corrected (L) transposition240.70.44110.50.320.730.36–1.49−0.1
Outflow tract defects
Tetralogy of Fallot2096.43.821245.43.610.940.76–1.18−0.2
D-transposition of the great arteries1615.02.95612.71.770.600.45–0.81*W−1.2
Double outlet right ventricle581.81.06361.61.050.990.65–1.500.0
Truncus arteriosus411.30.75140.60.410.540.30–1.00*W−0.3
Atrioventricular septal defect
(atrioventricular canal)
With Down syndrome732.21.34622.71.801.350.96–1.890.5
Without Down syndrome611.91.12472.11.371.230.84–1.790.3
Total anomalous pulmonary
venous return
391.20.71210.90.640.900.53–1.51−0.1
Ebstein anomaly311.00.5770.30.200.360.16–0.82*W−0.4
Right obstructive defects
Tricuspid atresia230.70.4290.40.230.550.25–1.24−0.2
Pulmonary atresia, intact septum290.90.53200.90.581.100.62–1.940.1
Pulmonic stenosis, atresia1895.83.461546.74.481.301.05–1.601.0
Peripheral pulmonary stenosis1344.12.451848.05.352.181.75–2.73*B2.9
Left obstructive defects
Hypoplastic left heart1073.31.96773.42.241.140.85–1.53−1.1
Coarctation of the aorta1825.63.33813.52.360.710.55–0.92*W1.8
Aortic arch atresia or hypoplasia331.00.60221.00.641.060.62–1.82−0.7
Aortic valve stenosis722.21.32170.70.490.380.22–0.64*W−16.0
Septal defects
Ventricular septal defect90427.916.5457425.116.691.010.91–1.1210.8
Atrial septal defect2106.53.842008.75.821.511.25–1.84*B0.3
Patent ductus arteriosus32410.05.9326211.57.621.291.09–1.51*B−51.7
Other major heart defects3029.35.5226611.67.741.401.19–1.65*B7.7
Total324510059.35228710066.511.121.06–1.18*B66.5
  • W indicates excess rate among whites; B, excess rate among blacks.

  • * Rate per 10 000 births.

  • Rate among blacks/rate among whites.

  • P < .05.

  • § Rate among blacks minus rate among whites.