PEDIATRICS Vol. 97 No. 2 February 1996, pp. 225-231
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Amyoplasia, the Most Common Type of Arthrogryposis: The Potential for Good Outcome

Jill M. Sells MD1, Kenneth M. Jaffe MD2, and Judith G. Hall MD3

1 The Department of Pediatrics, University of Washington and Children's Hospital and Medical Center, Seattle
2 The Departments of Pediatrics and Rehabilitation Medicine, University of Washington and Children's Hospital and Medical Center, Seattle
3 Departments of Pediatrics and Medical Genetics, University of British Columbia and British Columbia's Children's Hospital, Vancouver, British Columbia, Canada.

Background. Amyoplasia is the most commonly seen diagnostic subgroup of children with arthrogryposis. The natural history of these children has not been well described previously.

Methods. Review of the medical records of 38 children with amyoplasia enabled us to describe their birth characteristics, therapeutic interventions, and functional outcomes.

Results. Eighty-four percent of the children had symmetrical, four-limb involvement, which was similar to the original descriptions of amyoplasia, at birth. There was an average of 5.7 orthopedic procedures per child, and the children had multiple castings and splintings of their limbs and participated in physical and occupational therapy on a regular basis. By the age of 5 years, 85% were ambulatory, most were relatively or completely independent in their activities of daily living, and most were in regular classrooms at the appropriate grade level.

Conclusion. Although children with amyoplasia have pronounced musculoskeletal involvement at birth, which requires orthopedic and rehabilitative interventions during their childhood, their functional outcome in both physical and educational areas is excellent.

Key Words: amyoplasia • arthrogryposis • joint contractures

Submitted on December 6, 1994
Accepted on March 17, 1995




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