PEDIATRICS Vol. 91 No. 6 June 1993, pp. 1192-1194
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Congenital Microgastria and Limb Reduction Defects

CHRISTOPHER CUNNIFF MD1, LORI WILLIAMSON-KRUSE MS1, and ANN HASKINS OLNEY MD2

1 Dept of Pediatrics, University of Arkansas for Medical Sciences, Little Rock
2 Dept of Pediatrics, University of Nebraska Medical Center, Omaha

In 1842 Robert1 reported the case of a girl with microgastria; hypoplastic left forearm, hand, and wrist; and asplenia. Since that time, six additional patients with a similar pattern of malformation have been described.2-7 The purposes of this report are to describe three additional cases of the microgastria-limb reduction complex which illustrate the clinical variability of this condition, to discuss overlap of this disorder with other malformation syndromes and associations, and to present evidence that suggests that the microgastria-limb reduction complex represents a developmental field defect.

CLINICAL REPORTS

Patient 1

Patient 1 was evaluated at age 1 month for bilateral absent thumbs.

Submitted on November 2, 1992
Accepted on December 30, 1992