1 Center for Human Genetics, Massachusetts General Hospital and Children's Hospital Medical Center, and Division of Epidemiology and Biostatistics, Sidney Farber Cancer Institute, Harvard Medical School, and Clinical Studies Section, National Cancer Institute, Boston
Wilms tumor developed in five cousins in a family. Two with bilateral tumors have died, but three with unilateral lesions have survived. None of the patients had associated chromosome defects, aniridia, hemihypertrophy, or other anomalies. The pattern of Wilms tumor in the family is consistent with several postulated mechanisms of inheritance of the neoplasm, and shows that relatives within affected families may be at risk.
Submitted on December 14, 1979