PEDIATRICS Vol. 62 No. 3 September 1978, pp. 421-423
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Congenital Cystic Adenomatoid Malformation of the Lung Associated With Abdominal Musculature Deficiency (Prune Belly)

Stephen K. Wilson M.D.1, C. William Moore M.D., Ph.D.1, and Grover M. Hutchins M.D.1

1 Department of Pathology, The Johns Hopkins Medical Institutions Baltimore

"Prune belly"—a deficiency of abdominal niusculature usually associated with urinary tract anomalies and cryptorchidism—has been explained by numerous theories. Some postulate a primary defect of abdominal musculature, producing renal dysfunction1; others suggest the reverse2; other proposals include a sex-linked inherited trait3, and an intrauterine insult (between six and ten weeks of gestation).4

Congenital cystic adenomatoid malformation of the lung (CCAM) is a distinct morphological entity, characterized by a proliferation of cysts lined by bronchiolar-like epithelium and a lack of cartilage and seromucous glands.5 CCAM has been postulated to be a harnartoma,6 a focal type of pulmonary dysplasia,7 or a development anomaly.8