Congenital Cystic Adenomatoid Malformation of the Lung Associated With Abdominal Musculature Deficiency (Prune Belly)
1 Department of Pathology, The Johns Hopkins Medical Institutions Baltimore
"Prune belly"a deficiency of abdominal niusculature usually associated with urinary tract anomalies and cryptorchidismhas been explained by numerous theories. Some postulate a primary defect of abdominal musculature, producing renal dysfunction1; others suggest the reverse2; other proposals include a sex-linked inherited trait3, and an intrauterine insult (between six and ten weeks of gestation).4
Congenital cystic adenomatoid malformation of the lung (CCAM) is a distinct morphological entity, characterized by a proliferation of cysts lined by bronchiolar-like epithelium and a lack of cartilage and seromucous glands.5 CCAM has been postulated to be a harnartoma,6 a focal type of pulmonary dysplasia,7 or a development anomaly.8




