1 Department of Pathology, Tufts University School of Medicine and Dental Medicine, 136 Harrison Avenue, Boston, Massachusetts 02111
This report deals with a most unusual disease of the heart that was characterized clinically by irreversible atrial tachycardia and recurrent ventricular fibrillation. This led to the death of a 13-month-old female infant. Anatomically, xanthomatous clusters of closely packed lipid-containing cells displaced segments of the myocardium. Neither the etiology nor pathogenesis of this disease is known. This is the seventh such case to be recorded.