PEDIATRICS Vol. 46 No. 6 December 1970, pp. 929-933
This Article
Right arrow Full Text (PDF)
Right arrow P3Rs: Submit a response
Right arrow Alert me when this article is cited
Right arrow Alert me when P3Rs are posted
Right arrow Alert me if a correction is posted
Services
Right arrow E-mail this article to a friend
Right arrow Similar articles in this journal
Right arrow Similar articles in PubMed
Right arrow Alert me to new issues of the journal
Right arrow Add to My File Cabinet
Right arrow Download to citation manager
Right arrow reprints & permissions
Citing Articles
Right arrow Citing Articles via CrossRef
Right arrow Citing Articles via Google Scholar
Google Scholar
Right arrow Articles by Boley, S. J.
Right arrow Articles by Gliedman, M. L.
Right arrow Search for Related Content
PubMed
Right arrow PubMed Citation
Right arrow Articles by Boley, S. J.
Right arrow Articles by Gliedman, M. L.

Surgical Therapy of Glycogen Storage Disease

Scott J. Boley M.D.1, Michael I. Cohen M.D.1, and Marvin L. Gliedman M.D.1

1 Montefiore Hospital and Medical Center, Albert Einstein College of Medicine, Bronx, New York 10467

Portacaval shunt was successfully employed in the treatment of Type I glycogen storage disease. Severe hypoglycemia, acidosis, hyperlipidemia, and hyperuricemia were corrected and have not recurred although the child is on a regular diet without medication. Based upon our result and the limited experience of others, total portal venous diversion is recommended in early infancy in children with severe hypoglycemia before permanent cerebral damage has occurred.