STURGE-WEBER-DIMITRI DISEASE
Report of Case with Necropsy
1 Departments of Pathology, Neurosurgery and Pediatrics, Roger Williams General Hospital, Providence, Rhode Island
A case of Sturge-Weber's disease, confirmed by necropsy, in a female 2 3/12 years old, is presented.
This case, aside from its rarity, is noteworthy in that it is confirmed by necropsy, that the facial lesion is bilateral while the brain lesion is unilateral, and that there is an unusual amount of mineral deposit in the brain considering the short duration of the disease.
A general review of this interesting condition is presented.
As far as we have been able to tell, this case is the eighteenth confirmed case of Sturge-Weber's disease recorded in the American literature.
Submitted on January 11, 1958Accepted on February 28, 1958




