PEDIATRICS Vol. 12 No. 4 October 1953, pp. 368-376
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SYNDROME OF CONGENITAL HEMIHYPERTROPHY, SHORTNESS OF STATURE, AND ELEVATED URINARY GONADOTROPINS

HENRY K. SILVER M.D.1, WILLIAM KIYASU M.D.2, JACK GEORGE M.D.3, and WILLIAM C. DEAMER M.D.4

1 The Department of Pediatrics, Yale University School of Medicine, New Haven.
2 The Department of Pediatrics, University of California School of Medicine, San Francisco.
3 Children's Hospital, Boston.
4 Children's Hospital, Philadelphia.

Two cases of a syndrome of hemihypertrophy, shortness of stature, and elevated levels of urinary gonadotropins are reported. One of the children was a male, the other a female.

The hemihypertrophy and shortness of stature had been present since birth and the elevated gonadotropins were found at 5frac12 and 6 years, respectively.

The possible relationship to other conditions in childhood including those which also have increased gonadotropins is discussed.

Submitted on May 23, 1953




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